A rare cause of angina: scimitar syndrome case report

A 50-year-old woman presented to an outpatient cardiology clinic with a chief complaint of chest pain and dyspnoea on exertion. Physical exam was unrevealing. Chest radiograph showed prominence of the right pulmonary vasculature system in a characteristic curvilinear pattern suspicious for scimitar syndrome. Given this finding, electrocardiogram-gated coronary computed tomography angiography was obtained and demonstrated a large right pulmonary vein draining into the inferior vena cava (IVC), confirming the diagnosis of scimitar syndrome. Given her symptoms and a pulmonary-to-systemic flow > 2.14, the patient underwent surgical repair with creation of intra-atrial baffle to connect the anomalous right pulmonary vein to the left atrium. In the 9 years since her surgery, she reports complete resolution of her symptoms.

doi: doi.org/10.1093/ehjcr/ytad327 PMCID: PMC10404003